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Cerebellar Hypoplasia (Dandy Walker-like Malformation)
  • Description
  • Signalment
  • Clinical Features
  • Neurolocalization
  • Genetics
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A congenital malformation that is defined by inadequate development of the cerebellum. Causes can range from genetic abnormalities to in-utero infection. Concurrent hydrocephalus and hydranencephaly may also occur. It has been reported in several dogs with no breed predilection.
Age of Onset: 3 months of age
Sex Predisposition: Any sex of animal can be affected
Clinical Course:
​Clinical signs typically do not worsen over time
Clinical Signs:
Behavioral/Mental Awareness
Mental retardation
Seizures

Posture and Appearance  
Tremors
Shaking
Tonic neck

Movement
Ataxia
Hypermetria, more apparent in hindlimbs
Circling
Stumbling
Falling
Rhythmic dorsoventral bobbing of the head and trunk during elevation of the head

Proprioception
Proprioceptice deficits

Cranial Nerves
Absent menace response
Nystagmus
Strabismus

Special Reflexes (e.g. cutaneous trunci)  
Tonic eye reflexes

Other
May be associated with related vestibular abnormalities​
Cerebellum
Autosomal recessive VLDLR gene mutation

For breed specific genetic testing, click the link below:
https://www.genomia.cz/en/test/kombi-eurasier/
www.genomia.cz/en/test/cerebellar-hypoplasia/
​www.laboklin.co.uk/laboklin/showGeneticTest.jsp?testID=8260
To read more about this disease click below:
References
Picture
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