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Juvenile-Onset Polyneuropathy/Familial Nodo-Paranodal Polyneuropathy​
  • Description
  • Signalment
  • Clinical Features
  • Neurolocalization
  • Genetics
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Familial Nodo-paranodal polyneuropathy is an early onset neurodegenerative disorder of dogs.
Age of Onset: Early-onset; 1-6 months of age
Sex Predisposition: Any sex of animal can be affected
Clinical Course:
​Clinical signs begin with inspiratory dyspnea and ultimately progress to locomotor signs. Clinical signs are slowly progressive
Clinical Signs:
Posture and Appearance
Plantigrade/Palmigrade stance

Movement
Gait abnormalities
High-stepping gait
Ambulatory tetraparesis
Ataxia (pelvlic limbs > thoracic limbs)

​
Proprioception
Delayed postural reactions

Spinal Reflexes
Hyporeflexia

Special Functions (e.g. respiration; urination)
Laryngeal paralysis
Inspiratory stridor

Dyspnea
Regurgitation

Painful Reactions
Cutaneous hypoalgesia

Muscle Atrophy
Appendicular muscle atrophy
Peripheral nerves- mutlifocal
Suspected autosomal recessive inheritance
To read more about this disease click below:
References
Picture
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